Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV002034873 | SCV002107376 | pathogenic | not provided | 2022-03-17 | criteria provided, single submitter | clinical testing | Frameshift variant predicted to result in protein truncation, as the last 928 amino acids are replaced with 45 different amino acids, and other loss-of-function variants have been reported downstream in the Human Gene Mutation Database (HGMD); Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 30245513, 27133397) |