Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Revvity Omics, |
RCV003133782 | SCV003813943 | uncertain significance | Autosomal dominant intellectual disability-craniofacial anomalies-cardiac defects syndrome | 2019-08-06 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV003396907 | SCV004110901 | uncertain significance | KAT6A-related disorder | 2024-06-14 | no assertion criteria provided | clinical testing | The KAT6A c.3386G>A variant is predicted to result in the amino acid substitution p.Arg1129Gln. To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.00090% of alleles in individuals of European (Non-Finnish) descent in gnomAD. At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |