Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000521293 | SCV000620780 | uncertain significance | not provided | 2018-04-20 | criteria provided, single submitter | clinical testing | The V1992L variant in the KAT6A gene has not been reported previously as a pathogenic variant, nor as a benign variant, to our knowledge. The V1992L variant is not observed in large population cohorts (Lek et al., 2016). The V1992L variant is a conservative amino acid substitution, which is not likely to impact secondary protein structure as these residues share similar properties. This substitution occurs at a position that is conserved across species. In silico analysis is inconsistent in its predictions as to whether or not the variant is damaging to the protein structure/function. We interpret V1992L as a variant of uncertain significance. |