Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV004577075 | SCV005060875 | uncertain significance | Autosomal dominant intellectual disability-craniofacial anomalies-cardiac defects syndrome | criteria provided, single submitter | clinical testing | The splice region c.710-3T>C variant in KAT6A gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. This variant is absent in gnomAD Exomes and 1000 Genomes. This splice region variant in intron 3 affects the position three nucleotides upstream of exon 4. For these reasons, this variant has been classified as Uncertain Significance. |