Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV002467071 | SCV002762114 | likely pathogenic | not provided | 2022-06-07 | criteria provided, single submitter | clinical testing | Nonsense variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss of function is a known mechanism of disease; Not observed at significant frequency in large population cohorts (gnomAD); Has not been previously published as pathogenic or benign to our knowledge |
Baylor Genetics | RCV003464566 | SCV004191836 | likely pathogenic | LZTR1-related schwannomatosis | 2022-06-05 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV002467071 | SCV005796792 | pathogenic | not provided | 2024-11-12 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Gln568*) in the LZTR1 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in LZTR1 are known to be pathogenic (PMID: 24362817, 25335493, 25480913, 25795793, 29469822, 30368668, 30442762, 30442766, 30481304, 30859559). This variant is not present in population databases (gnomAD no frequency). This variant has not been reported in the literature in individuals affected with LZTR1-related conditions. ClinVar contains an entry for this variant (Variation ID: 1803401). For these reasons, this variant has been classified as Pathogenic. |