Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002602809 | SCV003497941 | uncertain significance | not provided | 2023-01-31 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is not expected to disrupt LZTR1 protein function. This variant has not been reported in the literature in individuals affected with LZTR1-related conditions. This variant is not present in population databases (gnomAD no frequency). This sequence change replaces phenylalanine, which is neutral and non-polar, with serine, which is neutral and polar, at codon 83 of the LZTR1 protein (p.Phe83Ser). |
Baylor Genetics | RCV003465975 | SCV004193672 | uncertain significance | Schwannomatosis 2 | 2023-05-01 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004560054 | SCV005047900 | uncertain significance | Hereditary cancer-predisposing syndrome; Cardiovascular phenotype | 2023-07-13 | criteria provided, single submitter | clinical testing | The p.F83S variant (also known as c.248T>C), located in coding exon 2 of the LZTR1 gene, results from a T to C substitution at nucleotide position 248. The phenylalanine at codon 83 is replaced by serine, an amino acid with highly dissimilar properties. This amino acid position is conserved. In addition, this alteration is predicted to be deleterious by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |