Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Women's Health and Genetics/Laboratory Corporation of America, |
RCV000586533 | SCV000698729 | benign | not provided | 2017-07-10 | criteria provided, single submitter | clinical testing | Variant summary: The LZTR1 c.450C>T (p.Asn150Asn) variant involves the alteration of a non-conserved nucleotide, resulting in a synonymous change. 5/5 splice prediction tools predict no significant impact on normal splicing. ESE finder predicts that this variant may not affect binding of ESE sites. This variant was found in 107/121282 control chromosomes (2 homozygotes) at a frequency of 0.0008822, which is approximately 176 times the estimated maximal expected allele frequency of a pathogenic LZTR1 variant (0.000005), suggesting this variant is likely a benign polymorphism. The variant of interest has not, to our knowledge, been reported in literature. Taken together, this variant is classified as benign. |
Labcorp Genetics |
RCV000586533 | SCV001717882 | benign | not provided | 2025-01-29 | criteria provided, single submitter | clinical testing | |
Genome Diagnostics Laboratory, |
RCV001813512 | SCV002060546 | benign | Noonan syndrome and Noonan-related syndrome | 2021-01-04 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002341503 | SCV002640116 | benign | Hereditary cancer-predisposing syndrome; Cardiovascular phenotype | 2020-09-02 | criteria provided, single submitter | clinical testing | This alteration is classified as benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Ce |
RCV000586533 | SCV005893847 | likely benign | not provided | 2024-12-01 | criteria provided, single submitter | clinical testing | LZTR1: BP4, BP7, BS2 |