Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Baylor Genetics | RCV003476462 | SCV004191230 | uncertain significance | Schwannomatosis 2 | 2023-10-13 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004560175 | SCV005048079 | uncertain significance | Hereditary cancer-predisposing syndrome; Cardiovascular phenotype | 2024-01-22 | criteria provided, single submitter | clinical testing | The p.C313S variant (also known as c.937T>A), located in coding exon 9 of the LZTR1 gene, results from a T to A substitution at nucleotide position 937. The cysteine at codon 313 is replaced by serine, an amino acid with dissimilar properties. This amino acid position is conserved. In addition, the in silico prediction for this alteration is inconclusive. Based on the available evidence, the clinical significance of this alteration remains unclear. |