Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000521491 | SCV000618430 | likely pathogenic | not provided | 2017-05-03 | criteria provided, single submitter | clinical testing | The I510S variant in the SYNGAP1 gene has not been reported previously as a pathogenic variant, nor as a benign variant, to our knowledge. It was identified as a de novo variant with confirmed parentage in a patient with seizures and intellectual disability previously tested at GeneDx. This variant is not observed in large population cohorts (Lek et al., 2016; 1000 Genomes Consortium et al., 2015; Exome Variant Server). The I510S variant is a non-conservative amino acid substitution that occurs at a position that is conserved across species, and in silico analysis predicts this variant is probably damaging to the protein structure/function. We interpret I510S as a likely pathogenic variant. |