Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Variantyx, |
RCV003110187 | SCV003761518 | likely pathogenic | Intellectual disability, autosomal dominant 5 | 2023-01-30 | criteria provided, single submitter | clinical testing | This is a nonsynonymous variant in the SYNGAP1 gene (OMIM: 603384). Pathogenic variants in this gene have been associated with autosomal dominant intellectual developmental disorder-5. This variant was identified de novo in this individual (PS2). Multiple computational algorithms predict a deleterious effect for this substitution (PP3). This variant is absent from control populations (https://gnomad.broadinstitute.org/) (PM2_Supporting). Based on the current evidence, this variant is classified as likely pathogenic for autosomal dominant intellectual developmental disorder-5 This variant has not been reported in individuals with SYNGAP1-related disorders in the databases available for review. |