Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Athena Diagnostics | RCV000992827 | SCV001145387 | uncertain significance | not provided | 2022-04-28 | criteria provided, single submitter | clinical testing | |
Gene |
RCV000992827 | SCV001779406 | uncertain significance | not provided | 2024-08-26 | criteria provided, single submitter | clinical testing | Has not been previously published as pathogenic or benign to our knowledge; In-frame deletion of 1 amino acid in a non-repeat region; In silico analysis supports a deleterious effect on protein structure/function |
Labcorp Genetics |
RCV000992827 | SCV004558260 | uncertain significance | not provided | 2023-01-27 | criteria provided, single submitter | clinical testing | This variant has not been reported in the literature in individuals affected with AFG3L2-related conditions. This variant is present in population databases (rs749105981, gnomAD 0.004%). This variant, c.1334_1336del, results in the deletion of 1 amino acid(s) of the AFG3L2 protein (p.Thr445del), but otherwise preserves the integrity of the reading frame. ClinVar contains an entry for this variant (Variation ID: 805323). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Experimental studies and prediction algorithms are not available or were not evaluated, and the functional significance of this variant is currently unknown. |