Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV003338212 | SCV004047230 | uncertain significance | Pontocerebellar hypoplasia type 10 | criteria provided, single submitter | clinical testing | The missense variant c.1214C>T (p.Ala405Val) in CLP1 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.Ala405Val variant is novel (not in any individuals) in 1000 Genomes and allele frequency of 0.00003987% is reported in gnomAD. The amino acid Ala at position 405 is changed to a Val changing protein sequence and it might alter its composition and physico-chemical properties. The amino acid change p.Ala405Val in CLP1 is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. For these reasons, this variant has been classified as Uncertain Significance. |