Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001268407 | SCV000681240 | pathogenic | not provided | 2020-03-25 | criteria provided, single submitter | clinical testing | Nonsense variant in the C-terminus predicted to result in protein truncation, as the last 53 amino acids are lost, and other loss-of-function variants have been reported downstream at GeneDx and in the Human Gene Mutation Database (Stenson et al., 2014); Not observed in large population cohorts (Lek et al., 2016); This variant is associated with the following publications: (PMID: 27479843, 29861108) |
SIB Swiss Institute of Bioinformatics | RCV000663347 | SCV000883264 | uncertain significance | Intellectual disability, autosomal dominant 57 | 2018-10-15 | criteria provided, single submitter | curation | This variant is interpreted as Uncertain Significance - Insufficient Evidence, for Mental retardation, autosomal dominant 57. The following ACMG Tag(s) were applied: PM2 => Absent from controls (or at extremely low frequency if recessive) in Exome Sequencing Project, 1000 Genomes Project, or Exome Aggregation Consortium. PM6 => Assumed de novo, but without confirmation of paternity and maternity (https://www.ncbi.nlm.nih.gov/pubmed/27479843) (https://www.ncbi.nlm.nih.gov/pubmed/29861108). |
Institute of Medical Genetics and Applied Genomics, |
RCV001268407 | SCV001447318 | likely pathogenic | not provided | 2020-10-23 | criteria provided, single submitter | clinical testing | |
OMIM | RCV000663347 | SCV000786618 | pathogenic | Intellectual disability, autosomal dominant 57 | 2022-04-29 | no assertion criteria provided | literature only |