Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000188047 | SCV000241650 | likely benign | not provided | 2021-05-18 | criteria provided, single submitter | clinical testing | Has not been previously published as pathogenic or benign to our knowledge; In silico analysis, which includes splice predictors and evolutionary conservation, suggests this variant may impact gene splicing. In the absence of RNA/functional studies, the actual effect of this sequence change is unknown. |
Labcorp Genetics |
RCV001080362 | SCV000652158 | benign | Lipoic acid synthetase deficiency | 2025-01-25 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV003917714 | SCV004733216 | likely benign | LIAS-related disorder | 2024-04-16 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |