Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001297112 | SCV001486098 | uncertain significance | not provided | 2022-09-14 | criteria provided, single submitter | clinical testing | This sequence change replaces methionine, which is neutral and non-polar, with isoleucine, which is neutral and non-polar, at codon 1084 of the SKIV2L protein (p.Met1084Ile). This variant is present in population databases (rs58092713, gnomAD 0.2%). This variant has not been reported in the literature in individuals affected with SKIV2L-related conditions. ClinVar contains an entry for this variant (Variation ID: 1000909). Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be tolerated. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Ambry Genetics | RCV004036058 | SCV004950923 | uncertain significance | Inborn genetic diseases | 2022-06-24 | criteria provided, single submitter | clinical testing | The c.3252G>A (p.M1084I) alteration is located in exon 26 (coding exon 26) of the SKIV2L gene. This alteration results from a G to A substitution at nucleotide position 3252, causing the methionine (M) at amino acid position 1084 to be replaced by an isoleucine (I). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
3billion | RCV004720302 | SCV005328802 | likely benign | Trichohepatoenteric syndrome 2 | 2024-09-20 | criteria provided, single submitter | clinical testing | The homozygous variant was found in patients diagnosed with another variant in a different gene, with no symptoms related to the gene containing the homozygous variant. |