Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
New York Genome Center | RCV002266644 | SCV002548681 | uncertain significance | Noonan syndrome 9 | 2021-07-16 | criteria provided, single submitter | clinical testing | The de novo c.*234G>A variant identified in the SOS2 gene is the substitution of a moderately conserved Cytosine for Thymine (at the DNA level) in the 3'UTR of SOS2. This variant is absent from gnomAD(v3.1.1) suggesting it is not a common benign variant in the populations represented in that database. This variant is absent from ClinVar and to our current knowledge has not been reported in affected individuals in the literature. While it is present de novo in the affected individual and absent in population databases, the lack of uncertainty regarding the functional consequence of the 3'UTR c.*234G>A variant identified in the SOS2 gene results in its classification as a Variant of Uncertain Significance. |