Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000033858 | SCV002229400 | pathogenic | Severe combined immunodeficiency due to CORO1A deficiency | 2022-08-19 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Pro83Argfs*11) in the CORO1A gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in CORO1A are known to be pathogenic (PMID: 18836449, 25073507). For these reasons, this variant has been classified as Pathogenic. ClinVar contains an entry for this variant (Variation ID: 40886). This premature translational stop signal has been observed in individual(s) with severe combined immunodeficiency (SCID) (PMID: 18836449, 27577878). In at least one individual the data is consistent with being in trans (on the opposite chromosome) from a pathogenic variant. This variant is not present in population databases (gnomAD no frequency). |
OMIM | RCV000033858 | SCV000057764 | pathogenic | Severe combined immunodeficiency due to CORO1A deficiency | 2014-10-01 | no assertion criteria provided | literature only |