Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clinical Genomics Laboratory, |
RCV005052275 | SCV005685397 | uncertain significance | Intellectual developmental disorder, autosomal dominant 63, with macrocephaly | 2024-12-13 | criteria provided, single submitter | clinical testing | The TRIO c.3406C>A (p.Gln1136Lys) variant, to our knowledge, has not been reported in the medical literature. This variant is absent from the general population (gnomAD v.2.1.1), indicating it is not a common variant. This variant resides within the spectrin repeat domain of TRIO (Gazdagh G et al., PMID: 36987741). Computational predictors are uncertain as to the impact of this variant on TRIO function. Due to limited information, and based on ACMG/AMP guidelines for variant interpretation (Richards S et al., PMID: 25741868), the clinical significance of this variant is uncertain at this time. |