Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002386961 | SCV002694212 | likely pathogenic | Hereditary cancer-predisposing syndrome | 2021-06-21 | criteria provided, single submitter | clinical testing | The c.966_967insSVA likely pathogenic variant results from the insertion of a SVA element between nucleotides 966 and 967 in coding exon 8 of the CHEK2 gene. Mobile element insertions contribute to pathogenicity by either disrupting the coding sequence or inducing aberrant splicing (Belancio VP et al. Semin. Cancer Biol. 2010 Aug;20:200-10; Deininger P et al. Genome Biol. 2011 Dec;12:236; van der Klift HM. Hum Mutat. 2012 Jul;33(7):1051-5). Based on the majority of available evidence to date, this variant is likely to be pathogenic. |