Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001546426 | SCV001765942 | likely pathogenic | not provided | 2019-12-27 | criteria provided, single submitter | clinical testing | Not observed at a significant frequency in large population cohorts (Lek et al., 2016); In silico analysis, which includes protein predictors and evolutionary conservation, supports a deleterious effect; This variant is associated with the following publications: (PMID: 27815843, 21786366) |
OMIM | RCV000023618 | SCV000044909 | pathogenic | Combined oxidative phosphorylation defect type 9 | 2011-11-01 | no assertion criteria provided | literature only |