Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics Munich, |
RCV003447443 | SCV004174814 | pathogenic | SNF8-associated disease | 2023-12-07 | criteria provided, single submitter | research | |
Ambry Genetics | RCV004364705 | SCV004952518 | uncertain significance | not specified | 2024-01-30 | criteria provided, single submitter | clinical testing | The c.304G>A (p.V102I) alteration is located in exon 4 (coding exon 4) of the SNF8 gene. This alteration results from a G to A substitution at nucleotide position 304, causing the valine (V) at amino acid position 102 to be replaced by an isoleucine (I). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
OMIM | RCV003994560 | SCV004812257 | pathogenic | Neurodevelopmental disorder plus optic atrophy | 2024-04-10 | no assertion criteria provided | literature only |