Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001924245 | SCV002206982 | uncertain significance | Autosomal recessive early-onset Parkinson disease 7 | 2021-09-20 | criteria provided, single submitter | clinical testing | Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Probably Damaging"; Align-GVGD: "Class C0"). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This variant has not been reported in the literature in individuals affected with PARK7-related conditions. This variant is present in population databases (rs761919138, ExAC 0.003%). This sequence change replaces valine with glycine at codon 146 of the PARK7 protein (p.Val146Gly). The valine residue is highly conserved and there is a moderate physicochemical difference between valine and glycine. |