Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Invitae | RCV000699924 | SCV000828655 | uncertain significance | Autosomal recessive early-onset Parkinson disease 7 | 2018-03-05 | criteria provided, single submitter | clinical testing | This variant has not been reported in the literature in individuals with PARK7-related disease. Algorithms developed to predict the effect of missense changes on protein structure and function do not agree on the potential impact of this missense change (SIFT: "Tolerated"; PolyPhen-2: "Possibly Damaging"; Align-GVGD: "Class C0"). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This variant is present in population databases (rs368420490, ExAC 0.02%). This sequence change replaces glycine with serine at codon 150 of the PARK7 protein (p.Gly150Ser). The glycine residue is moderately conserved and there is a small physicochemical difference between glycine and serine. |