Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
ARUP Laboratories, |
RCV001217811 | SCV000883697 | uncertain significance | Hereditary pancreatitis | 2024-07-25 | criteria provided, single submitter | clinical testing | The CTRC c.550G>A; p.Ala184Thr variant (rs761546594, ClinVar Variation ID: 618054), is reported in the literature in an individual affected with chronic pancreatitis (Stefanovics 2024). This variant is found in the general population with an overall allele frequency of 0.012% (33/282,812 alleles) in the Genome Aggregation Database (v2.1.1). Computational analyses are uncertain whether this variant is neutral or deleterious (REVEL: 0.217). Functional analyses of the variant protein show similar secretion and activity compared to wild type (Stefanovics 2024). Due to limited information, the clinical significance of the p.Ala184Thr variant is uncertain at this time. References: Stefanovics R et al. Novel chymotrypsin C (CTRC) variants from real-world genetic testing of pediatric chronic pancreatitis cases. Pancreatology. 2024 Aug;24(5):690-697. PMID: 38876922. |
Labcorp Genetics |
RCV001217811 | SCV001389663 | likely benign | Hereditary pancreatitis | 2024-09-12 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV001217811 | SCV002653547 | uncertain significance | Hereditary pancreatitis | 2024-04-13 | criteria provided, single submitter | clinical testing | The p.A184T variant (also known as c.550G>A), located in coding exon 6 of the CTRC gene, results from a G to A substitution at nucleotide position 550. The alanine at codon 184 is replaced by threonine, an amino acid with similar properties. This amino acid position is poorly conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |