Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
ARUP Laboratories, |
RCV001287787 | SCV001474517 | likely benign | Hereditary pancreatitis | 2020-12-24 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001287787 | SCV002406272 | benign | Hereditary pancreatitis | 2023-12-29 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV001287787 | SCV002660218 | uncertain significance | Hereditary pancreatitis | 2014-05-27 | criteria provided, single submitter | clinical testing | The c.640-14C>T intronic variant results from a C to T substitution 14 nucleotides upstream from coding exon 7 in the CTRC gene. This variant was previously reported in the SNPDatabase as rs202049497. Based on data from the 1000 Genomes Project, the T allele has an overall frequency of approximately 0.09% (2/2184) total alleles studied. The highest observed frequency was 0.91% (1/110) Puerto Rican alleles. Based on data from the NHLBI Exome Sequencing Project (ESP), the T allele has an overall frequency of approximately 0.1% (13/13006) total alleles studied, having been observed in 0.3% (13/4406) African American alleles. This nucleotide position is not conserved in available vertebrate species, and the T-allele is present in multiple species. Using the BDGP and ESEfinder splice site prediction tools, this alteration is not predicted to have any significant effect on this acceptor splice site; however, direct evidence is unavailable. Since supporting evidence is limited at this time, the clinical significance of this variant remains unclear. |
Prevention |
RCV003973185 | SCV004789178 | likely benign | CTRC-related disorder | 2019-05-01 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |