Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Fulgent Genetics, |
RCV005020352 | SCV005647130 | uncertain significance | Breast-ovarian cancer, familial, susceptibility to, 1; Pancreatic cancer, susceptibility to, 4; Fanconi anemia, complementation group S | 2024-02-28 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV005323681 | SCV005980090 | uncertain significance | Hereditary cancer-predisposing syndrome | 2025-01-06 | criteria provided, single submitter | clinical testing | The p.C1501F variant (also known as c.4502G>T), located in coding exon 13 of the BRCA1 gene, results from a G to T substitution at nucleotide position 4502. The cysteine at codon 1501 is replaced by phenylalanine, an amino acid with highly dissimilar properties. This amino acid position is conserved. In addition, the in silico prediction for this alteration is inconclusive. Based on the available evidence, the clinical significance of this variant remains unclear. |
Color Diagnostics, |
RCV005323681 | SCV006064113 | uncertain significance | Hereditary cancer-predisposing syndrome | 2023-08-15 | criteria provided, single submitter | clinical testing | This missense variant replaces cysteine with phenylalanine at codon 1501 of the BRCA1 protein. Computational prediction is inconclusive regarding the impact of this variant on protein structure and function (internally defined REVEL score threshold 0.5 < inconclusive < 0.7, PMID: 27666373). To our knowledge, functional studies have not been reported for this variant. This variant has not been reported in individuals affected with BRCA1-related disorders in the literature. This variant has not been identified in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |