Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000214759 | SCV000275204 | likely benign | Hereditary cancer-predisposing syndrome | 2020-07-16 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Color Diagnostics, |
RCV000214759 | SCV001345184 | uncertain significance | Hereditary cancer-predisposing syndrome | 2019-06-15 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001245538 | SCV001418833 | uncertain significance | Hereditary breast ovarian cancer syndrome | 2023-05-16 | criteria provided, single submitter | clinical testing | This variant is present in population databases (no rsID available, gnomAD 0.007%). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Experimental studies have shown that this missense change does not substantially affect BRCA1 function (PMID: 30209399). Advanced modeling performed at Invitae incorporating data from internal and/or published experimental studies (PMID: 30209399) indicates that this missense variant is not expected to disrupt BRCA1 function. ClinVar contains an entry for this variant (Variation ID: 231376). This variant has not been reported in the literature in individuals affected with BRCA1-related conditions. This sequence change replaces valine, which is neutral and non-polar, with isoleucine, which is neutral and non-polar, at codon 1741 of the BRCA1 protein (p.Val1741Ile). |
Brotman Baty Institute, |
RCV001076641 | SCV001242430 | not provided | Breast-ovarian cancer, familial, susceptibility to, 1 | no assertion provided | in vitro |