Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000509766 | SCV000607892 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-09-17 | criteria provided, single submitter | clinical testing | The p.S316N variant (also known as c.947G>A), located in coding exon 9 of the BRCA1 gene, results from a G to A substitution at nucleotide position 947. The serine at codon 316 is replaced by asparagine, an amino acid with highly similar properties. This amino acid position is highly conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Quest Diagnostics Nichols Institute San Juan Capistrano | RCV000758854 | SCV000887741 | uncertain significance | not provided | 2018-02-02 | criteria provided, single submitter | clinical testing | |
Molecular Endocrinology Laboratory, |
RCV001788270 | SCV002030311 | uncertain significance | Breast-ovarian cancer, familial, susceptibility to, 1 | criteria provided, single submitter | clinical testing | ||
University of Washington Department of Laboratory Medicine, |
RCV000509766 | SCV003846274 | likely benign | Hereditary cancer-predisposing syndrome | 2023-03-23 | criteria provided, single submitter | curation | Missense variant in a coldspot region where missense variants are very unlikely to be pathogenic (PMID:31911673). |
Neuberg Centre For Genomic Medicine, |
RCV001788270 | SCV005849021 | uncertain significance | Breast-ovarian cancer, familial, susceptibility to, 1 | 2023-06-22 | criteria provided, single submitter | clinical testing | The missense variant c.947G>A (p.Ser316Asn) in the BRCA1 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. This variant is reported with the allele frequency (0.0003%) in the gnomAD Exomes. This variant has been reported to the ClinVar database as Uncertain Significance/ Likely Benign. However, no details are available for independent assessment. The amino acid Ser at position 316 is changed to a Asn changing protein sequence and it might alter its composition and physico-chemical properties. Multiple lines of computational evidence (Polyphen - Damaging and MutationTaster - Disease causing) predict a damaging effect on protein structure and function for this variant. The amino acid change p.Ser316Asn in BRCA1 is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. For these reasons, this variant has been classified as Uncertain Significance. |