Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV004823553 | SCV005442735 | pathogenic | Intellectual disability, autosomal dominant 8 | 2025-01-06 | criteria provided, single submitter | clinical testing | Criteria applied: PS2_MOD, PS3, PM1, PM2, PP2, PP3. This variant was identified as de novo (maternity and paternity confirmed). Functional analysis performed by the Center of Functional Evaluation of Rare Variants (CVERV, Traynelis Lab, Emory) showed a "likely Gain-of-function" effect of the variant on the NMDAR, see https://grin-portal.broadinstitute.org/ |