Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV003337907 | SCV004048328 | uncertain significance | Parkinsonian-pyramidal syndrome | criteria provided, single submitter | clinical testing | The missense variant c.52G>A (p.Glu18Lys) in FBXO7 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. This variant is reported with the allele frequency (0.0007%) in the gnomad and novel in 1000 genome database. The amino acid Glutamic acid at position 18 is changed to a Lysine changing protein sequence and it might alter its composition and physico-chemical properties. In silico tools predict the variant to be tolerated. The residue is conserved across species. For these reasons, this variant has been classified as Uncertain Significance. |