Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Mayo Clinic Laboratories, |
RCV000660582 | SCV000782694 | uncertain significance | not provided | 2017-06-23 | criteria provided, single submitter | clinical testing | |
Gene |
RCV000660582 | SCV005332330 | likely pathogenic | not provided | 2023-11-13 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 34930816, 33144682) |
Institute of Human Genetics, |
RCV004760682 | SCV005368271 | likely pathogenic | Neurodevelopmental disorder with language delay and behavioral abnormalities, with or without seizures | 2024-08-09 | criteria provided, single submitter | clinical testing | Criteria applied: PS2_MOD,PM1,PS4_SUP,PM2_SUP |