Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000695666 | SCV000824180 | uncertain significance | Bardet-Biedl syndrome | 2018-03-01 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function do not agree on the potential impact of this missense change (SIFT: "Tolerated"; PolyPhen-2: "Benign"; Align-GVGD: "Class C25"). This variant has not been reported in the literature in individuals with TRIM32-related disease. This variant is present in population databases (rs771427815, ExAC 0.01%). This sequence change replaces alanine with serine at codon 348 of the TRIM32 protein (p.Ala348Ser). The alanine residue is moderately conserved and there is a moderate physicochemical difference between alanine and serine. |