Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Eurofins Ntd Llc |
RCV000369921 | SCV000336525 | uncertain significance | not provided | 2017-12-11 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000460669 | SCV000552163 | uncertain significance | Bardet-Biedl syndrome | 2022-09-06 | criteria provided, single submitter | clinical testing | This sequence change replaces proline, which is neutral and non-polar, with leucine, which is neutral and non-polar, at codon 329 of the TRIM32 protein (p.Pro329Leu). This variant is present in population databases (rs377510422, gnomAD 0.01%). This variant has not been reported in the literature in individuals affected with TRIM32-related conditions. ClinVar contains an entry for this variant (Variation ID: 284059). Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Benign"; Align-GVGD: "Class C15"). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Fulgent Genetics, |
RCV002480017 | SCV002788002 | uncertain significance | Sarcotubular myopathy; Bardet-Biedl syndrome 11 | 2024-03-07 | criteria provided, single submitter | clinical testing | |
Revvity Omics, |
RCV000369921 | SCV003823469 | uncertain significance | not provided | 2023-06-14 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV004748690 | SCV005348182 | uncertain significance | TRIM32-related disorder | 2024-09-24 | no assertion criteria provided | clinical testing | The TRIM32 c.986C>T variant is predicted to result in the amino acid substitution p.Pro329Leu. To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.014% of alleles in individuals of Latino descent in gnomAD. At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |