Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Mendelics | RCV002247916 | SCV002517227 | uncertain significance | not specified | 2022-05-04 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV003093982 | SCV003252945 | uncertain significance | Early myoclonic encephalopathy | 2023-07-10 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Experimental studies have shown that this missense change affects KCND2 function (PMID: 25214526). This sequence change replaces aspartic acid, which is acidic and polar, with asparagine, which is neutral and polar, at codon 612 of the KCND2 protein (p.Asp612Asn). This variant is present in population databases (rs151258092, gnomAD 0.01%). This missense change has been observed in individual(s) with J-wave syndrome (PMID: 25214526). ClinVar contains an entry for this variant (Variation ID: 1684824). Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is not expected to disrupt KCND2 protein function. |