Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001949358 | SCV002237819 | pathogenic | Early myoclonic encephalopathy | 2021-09-10 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is expected to disrupt KCND2 protein function. This missense change has been observed in individual(s) with clinical features of epilepsy and autism spectrum disorder (Invitae). In at least one individual the variant was observed to be de novo. This variant is not present in population databases (ExAC no frequency). This sequence change replaces arginine with cysteine at codon 305 of the KCND2 protein (p.Arg305Cys). The arginine residue is highly conserved and there is a large physicochemical difference between arginine and cysteine. |