Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV003333816 | SCV004041604 | likely pathogenic | Genitopatellar syndrome | 2023-10-10 | criteria provided, single submitter | clinical testing | The KAT6B-variant NM_001256468.2:c.4453A>G is classified by our institute as a likely pathogenic variant, as it is not present in any databases (gnomAD / ExAC), as a missense effect, what is a known pathomechanism for the associated disease, and the majority of the prediction programs used judge the variant to be damaging. The clinical symptoms of the patient fit to known symptoms for the associated diseases. The patient's parents do not carry the variant (in the case of nonproven parenthood). |