Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002873139 | SCV003620444 | uncertain significance | Inborn genetic diseases | 2022-06-08 | criteria provided, single submitter | clinical testing | The c.2090A>G (p.N697S) alteration is located in exon 20 (coding exon 20) of the RAB3GAP2 gene. This alteration results from a A to G substitution at nucleotide position 2090, causing the asparagine (N) at amino acid position 697 to be replaced by a serine (S). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Revvity Omics, |
RCV003491280 | SCV004236529 | uncertain significance | not provided | 2023-11-07 | criteria provided, single submitter | clinical testing | |
Neuberg Centre For Genomic Medicine, |
RCV005208198 | SCV005849252 | uncertain significance | Warburg micro syndrome 2 | criteria provided, single submitter | clinical testing | The missense c.2090A>G (p.Asn697Ser) variant in RAB3GAP2 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.Asn697Ser variant is present with allele frequency of 0.0008% in gnomAD Exomes. This variant has been submitted to the ClinVar database as Uncertain Significance. Multiple lines of computational evidence (Polyphen - Benign, SIFT - Tolerated and MutationTaster - Polymorphism) predict no damaging effect on protein structure and function for this variant. The reference amino acid at this position on RAB3GAP2 is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. The amino acid Asn at position 697 is changed to a Ser changing protein sequence and it might alter its composition and physico-chemical properties. For these reasons, this variant has been classified as a Variant of Uncertain Significance (VUS). |