Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001360494 | SCV001556414 | uncertain significance | CHARGE syndrome | 2022-08-23 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function output the following: SIFT: "Tolerated"; PolyPhen-2: "Benign"; Align-GVGD: "Class C0". The histidine amino acid residue is found in multiple mammalian species, which suggests that this missense change does not adversely affect protein function. ClinVar contains an entry for this variant (Variation ID: 1052334). This variant has not been reported in the literature in individuals affected with SEMA3E-related conditions. This variant is present in population databases (rs140160399, gnomAD 0.02%). This sequence change replaces arginine, which is basic and polar, with histidine, which is basic and polar, at codon 619 of the SEMA3E protein (p.Arg619His). |
Fulgent Genetics, |
RCV002486508 | SCV002783710 | uncertain significance | CHARGE syndrome; Hypogonadotropic hypogonadism 7 with or without anosmia | 2021-12-29 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV003416260 | SCV004106552 | uncertain significance | SEMA3E-related disorder | 2024-07-24 | no assertion criteria provided | clinical testing | The SEMA3E c.1856G>A variant is predicted to result in the amino acid substitution p.Arg619His. To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.016% of alleles in individuals of African descent in gnomAD. Although we suspect that this variant may be benign, at this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |