Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Cardiogenetic Research Center, |
RCV001260955 | SCV001244255 | likely pathogenic | Salla disease | 2019-12-05 | criteria provided, single submitter | research | |
Gene |
RCV004726874 | SCV005333231 | likely pathogenic | not provided | 2024-02-22 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 33547378, 36662855) |
Myelin Disorders Clinic- |
RCV001090089 | SCV001244901 | uncertain significance | Sialic acid storage disease, severe infantile type | no assertion criteria provided | clinical testing |