Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Paediatric Endocrinology - |
RCV000625735 | SCV000693651 | pathogenic | Growth hormone insensitivity with immune dysregulation 1, autosomal recessive | 2017-08-02 | no assertion criteria provided | research | Functional studies have shown that the Stat5b variant results in reduced DNA binding. The Stat5b variant segregated in this family with the phenotype of short stature. |
OMIM | RCV001254779 | SCV001430881 | pathogenic | Growth hormone insensitivity syndrome with immune dysregulation 2, autosomal dominant | 2020-08-24 | no assertion criteria provided | literature only |