Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
ARUP Laboratories, |
RCV000756793 | SCV000884706 | uncertain significance | not provided | 2017-10-10 | criteria provided, single submitter | clinical testing | The p.Arg202Cys variant (rs143562358) has not been reported in the medical literature, gene specific variation databases, nor has it been previously identified by our laboratory. Another change at this position p.Arg202His has been reported in associated with common variable immunodeficiency (Salzer 2005). However, the p.Arg202His variant was later found in control populations and did no segregate with disease in patients with selective IgA deficiency (Pan-Hammarstrom 2007). The p.Arg202Cys variant is listed in the genome Aggregation Database (gnomAD) with an African population frequency of 0.13 percent (identified on 31 out of 24,002 chromosomes). The arginine at position 202 is weakly conserved (considering 10 species, Alamut v.2.10.0) and Rhesus and other species have cysteine at this position indicating this change may be evolutionarily tolerated. Computational analyses of the effects of the p.Arg202Cys variant on protein structure and function indicated a neutral effect (SIFT: tolerated, MutationTaster: polymorphism, PolyPhen-2: benign). Altogether, there is not enough evidence to classify the p.Arg202Cys variant with certainty. |
Labcorp Genetics |
RCV000801725 | SCV000941517 | likely benign | Immunodeficiency, common variable, 2 | 2025-01-29 | criteria provided, single submitter | clinical testing | |
Mayo Clinic Laboratories, |
RCV000756793 | SCV001712899 | uncertain significance | not provided | 2019-04-07 | criteria provided, single submitter | clinical testing | |
New York Genome Center | RCV000801725 | SCV001761121 | uncertain significance | Immunodeficiency, common variable, 2 | 2020-06-26 | criteria provided, single submitter | clinical testing |