Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Blueprint Genetics | RCV000208496 | SCV000263822 | uncertain significance | Primary familial hypertrophic cardiomyopathy | 2015-09-30 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001853297 | SCV002142452 | uncertain significance | Arrhythmogenic right ventricular dysplasia 13 | 2022-11-01 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Gln78*) in the CTNNA3 gene. It is expected to result in an absent or disrupted protein product. However, the current clinical and genetic evidence is not sufficient to establish whether loss-of-function variants in CTNNA3 cause disease. This variant is present in population databases (rs201306690, gnomAD 0.02%). This variant has not been reported in the literature in individuals affected with CTNNA3-related conditions. ClinVar contains an entry for this variant (Variation ID: 222536). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |