Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002317981 | SCV000849545 | likely benign | Inborn genetic diseases | 2020-09-17 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
New York Genome Center | RCV001862052 | SCV001468818 | uncertain significance | KBG syndrome | 2019-06-21 | criteria provided, single submitter | clinical testing | |
Gene |
RCV001556943 | SCV001778617 | likely benign | not provided | 2021-05-10 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001862052 | SCV002317329 | uncertain significance | KBG syndrome | 2025-01-28 | criteria provided, single submitter | clinical testing | This sequence change replaces serine, which is neutral and polar, with leucine, which is neutral and non-polar, at codon 588 of the ANKRD11 protein (p.Ser588Leu). This variant is present in population databases (rs202142344, gnomAD 0.01%). This variant has not been reported in the literature in individuals affected with ANKRD11-related conditions. ClinVar contains an entry for this variant (Variation ID: 589037). Invitae Evidence Modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) indicates that this missense variant is not expected to disrupt ANKRD11 protein function with a negative predictive value of 95%. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |