Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002318072 | SCV000849728 | uncertain significance | Inborn genetic diseases | 2017-05-28 | criteria provided, single submitter | clinical testing | The c.6063_6071delTCCTGCCCC variant (also known as p.P2022_P2024del) is located in coding exon 7 of the ANKRD11 gene. This variant results from an in-frame TCCTGCCCC deletion at nucleotide positions 6063 to 6071. This results in the in-frame deletion of PAP at codons 2022 to 2024. These amino acid positions are conserved on limited sequence alignment. In addition, this alteration is predicted to be neutral by PROVEAN in silico analysis (Choi Y et al., PLoS ONE 2012; 7(10):e46688). Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Gene |
RCV003327455 | SCV004034772 | uncertain significance | not provided | 2023-03-07 | criteria provided, single submitter | clinical testing | In-frame deletion of 3 amino acids in a non-repeat region; In silico analysis supports that this variant does not alter protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |
Labcorp Genetics |
RCV003525953 | SCV004353362 | uncertain significance | KBG syndrome | 2024-09-04 | criteria provided, single submitter | clinical testing | This variant, c.6063_6071del, results in the deletion of 3 amino acid(s) of the ANKRD11 protein (p.Pro2022_Pro2024del), but otherwise preserves the integrity of the reading frame. This variant is present in population databases (rs771037147, gnomAD 0.01%). This variant has not been reported in the literature in individuals affected with ANKRD11-related conditions. ClinVar contains an entry for this variant (Variation ID: 589132). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |