Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ce |
RCV000761964 | SCV000892192 | uncertain significance | not provided | 2018-04-01 | criteria provided, single submitter | clinical testing | |
Genetics and Molecular Pathology, |
RCV002272345 | SCV002556736 | uncertain significance | KBG syndrome | 2021-05-10 | criteria provided, single submitter | clinical testing | The ANKRD11 c.7753C>T variant is classified as a VARIANT OF UNCERTAIN SIGNIFICANCE (PM2, PP3) The ANKRD11 c.7753C>T variant is a single nucleotide change in exon 13 of the ANKRD11 gene, which is predicted to change the amino acid arginine at position 2585 in the protein to cysteine. This variant has not been reported in dbSNP and is absent from population databases (PM2). This variant has been reported in ClinVar as a variant of uncertain significance (ClinVar Variation ID: 613051). This variant has not been reported in HGMD. Computational predictions support a deleterious effect on the gene or gene product (PP3). |
Gene |
RCV000761964 | SCV003762084 | pathogenic | not provided | 2023-01-22 | criteria provided, single submitter | clinical testing | Published functional studies demonstrate a damaging effect (PMID: 35833929); Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 35833929, 36446582) |