Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002512640 | SCV003523905 | uncertain significance | not provided | 2022-10-09 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Experimental studies have shown that this variant affects LAMTOR2 function (PMID: 17195838). Algorithms developed to predict the effect of variants on protein structure and function are not available or were not evaluated for this variant. ClinVar contains an entry for this variant (Variation ID: 1239). This variant has been observed in individual(s) with immunodeficiency (PMID: 17195838). This variant is present in population databases (no rsID available, gnomAD 0.002%). This variant occurs in a non-coding region of the LAMTOR2 gene. It does not change the encoded amino acid sequence of the LAMTOR2 protein. |
OMIM | RCV000001298 | SCV000021448 | pathogenic | Primary immunodeficiency syndrome due to p14 deficiency | 2007-01-01 | no assertion criteria provided | literature only |