Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000546888 | SCV000645107 | uncertain significance | Cortical dysplasia-focal epilepsy syndrome | 2017-01-23 | criteria provided, single submitter | clinical testing | Algorithms developed to predict the effect of missense changes on protein structure and function do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Benign"; Align-GVGD: "Class C0"). In summary, this variant is a novel missense change with uncertain impact on protein function. It has been classified as a Variant of Uncertain Significance. This variant is not present in population databases (ExAC no frequency) and has not been reported in the literature in individuals with a CNTNAP2-related disease. This sequence change replaces threonine with asparagine at codon 1144 of the CNTNAP2 protein (p.Thr1144Asn). The threonine residue is highly conserved and there is a small physicochemical difference between threonine and asparagine. |