Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV001265983 | SCV001444155 | uncertain significance | Inborn genetic diseases | 2020-03-09 | criteria provided, single submitter | clinical testing | The alteration results in an amino acid change:_x000D_ _x000D_ The c.221C>T (p.A74V) alteration is located in coding exon 3 of the VAMP2 gene. This alteration results from a C to T substitution at nucleotide position 221, causing the alanine (A) at amino acid position 74 to be replaced by a valine (V). The alteration is not observed in population databases: _x000D_ _x000D_ Based on data from the Genome Aggregation Database (gnomAD), the VAMP2 c.221 C>T alteration was not observed, with coverage at this position. The altered amino acid is conserved throughout evolution:_x000D_ _x000D_ The p.A74 amino acid is conserved in available vertebrate species. The alteration is predicted inconclusive by in silico modeling:_x000D_ _x000D_ The in silico prediction for the p.A74V alteration is inconclusive. Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Undiagnosed Diseases Network, |
RCV001310231 | SCV001499844 | uncertain significance | Neurodevelopmental disorder with hypotonia and autistic features with or without hyperkinetic movements | 2020-04-09 | criteria provided, single submitter | clinical testing |