Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002048629 | SCV002307006 | pathogenic | not provided | 2022-08-15 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may disrupt the consensus splice site. ClinVar contains an entry for this variant (Variation ID: 1515844). This variant has been observed in individuals with clinical features of congenital myopathy (Invitae). This variant is not present in population databases (gnomAD no frequency). This variant results in the deletion of part of exon 2 (c.373_375+2del) of the HACD1 gene. It is expected to disrupt RNA splicing. Variants that disrupt the donor or acceptor splice site typically lead to a loss of protein function (PMID: 16199547), and loss-of-function variants in HACD1 are known to be pathogenic (PMID: 23933735). |
OMIM | RCV002271315 | SCV002553210 | pathogenic | Congenital myopathy 11 | 2024-07-16 | no assertion criteria provided | literature only |