Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratorio de Genetica e Diagnostico Molecular, |
RCV002252623 | SCV002523977 | likely pathogenic | See cases | 2021-03-28 | criteria provided, single submitter | clinical testing | ACMG classification criteria: PVS1, PM2 |
DASA | RCV002300657 | SCV002588760 | pathogenic | Joubert syndrome 25 | 2022-11-03 | criteria provided, single submitter | clinical testing | The c.1879G>T;p.(Glu627*) variant creates a premature translational stop signal in the CEP104 gene. It is expected to result in an absent or disrupted protein product - PVS1. ClinVar contains an entry for this variant (ClinVar ID: 1691031) - PS4_supporting. This variant is not present in population databases (rs750473230, gnomAD; ABraOM no frequency - http://abraom.ib.usp.br/) - PM2. In summary, the currently available evidence indicates that the variant is pathogenic. |